missing translation for 'onlineSavingsMsg'
Learn More
Learn More
branched chain keto acid dehydrogenase E1, alpha polypeptide, Mouse, Polyclonal Antibody, Abnova™
Mouse polyclonal antibody raised against a partial recombinant BCKDHA.
Brand: Abnova H00000593-A01.50uL
This item is not returnable.
View return policy
Description
The branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex is an innter mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). This gene encodes the alpha subunit of the decarboxylase (E1) component. Mutations in this gene result in maple syrup urine disease, type IA. Multiple transcript variants encoding different isoforms have been found for this gene
Sequence: SVDEVNYWDKQDHPISRLRHYLLSQGWWDEEQEKAWRKQSRRKVMEAFEQAERKPKPNPNLLFSDVYQEMPAQLRKQQESLARHLQTYGEHYPLDHFDKSpecifications
| branched chain keto acid dehydrogenase E1, alpha polypeptide | |
| Polyclonal | |
| Mouse polyclonal antibody raised against a partial recombinant BCKDHA. | |
| BCKDHA | |
| BCKDE1A/FLJ45695/MSU/MSUD1/OVD1A | |
| Mouse | |
| 50 μL | |
| Yes | |
| 593 | |
| Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing. |
| ELISA, Western Blot | |
| Unconjugated | |
| 50% glycerol | |
| NM_000709 | |
| BCKDHA | |
| BCKDHA (NP_000700, 347 a.a. ∼ 445 a.a) partial recombinant protein with GST tag. | |
| RUO | |
| Primary | |
| Human | |
| Serum |
Product Content Correction
Your input is important to us. Please complete this form to provide feedback related to the content on this product.
Product Title
Spot an opportunity for improvement?Share a Content Correction